Auditory neuropathy in a patient with hemochromatosis

auditory neuropathy and auditory neuropathy spectrum disorders

editorial

Auditory neuropathy in a patient exposed to xylene: case report.

OBJECTIVE To report the case of an adult patient who developed auditory complaints following xylene exposure, and to review the literature on the effects of solvent exposure on hearing. CASE REPORT The patient presented with a gradual deterioration in his ability to hear in difficult acoustic environments and also to hear complex sounds such as music, over a 40-year period. His symptoms began...

Progressive auditory neuropathy in patients with Leber's hereditary optic neuropathy.

OBJECTIVE To investigate auditory neural involvement in patients with Leber's hereditary optic neuropathy (LHON). METHODS Auditory assessment was undertaken in two patients with LHON. One was a 45 year old woman with Harding disease (multiple-sclerosis-like illness and positive 11778mtDNA mutation) and mild auditory symptoms, whose auditory function was monitored over five years. The other wa...

Auditory neuropathy/Auditory dyssynchrony in children with Cochlear Implants.

UNLABELLED The electrical stimulation generated by the Cochlear Implant (CI) may improve the neural synchrony and hence contribute to the development of auditory skills in patients with Auditory Neuropathy/Auditory Dyssynchrony (AN/AD). AIM Prospective cohort cross-sectional study to evaluate the auditory performance and the characteristics of the electrically evoked compound action potential...

Reversible cardiomyopathy in a patient with juvenile hemochromatosis.